a fimine feed Metabolism
— file ence ee =
: late af Urea :
1. Ueea_dirfluses fear liver £ is - arene aes (a2. ging
to ue athece itis Giltred & exceed 'n usine.
2. poten of usta. dicfhacer fro Ble) Sabe the ioleshne
_.&.fs_cleaved +. C02 £2 NH3 by bacterial Ucease .
_this| ammonia is. partly last in Feces 2. is. pelesies
i the. blowd. arenes : ee
een Lamine (: Soure 2 Bislgic vale Bs ee fy ie pee
ioe is ftacmed by ae bskdine—
prquercouires LON a
ale cellular mspoases + _
6 2Kaf lam matory. mmachoas.
Fee MA ey ee eh
eee
_ 3. qreuotansmiscieng in parts «£ Beary.
__ 4. Seeotonin C sources £ physinlegic ale) cs
synthesized tm Tryphp han- 5
oalt ple hy salen voles: —
Tempecetire.
or : Bleed Pressure seca
aa Lad. (Boling eC evel - being
® |—. 5|Phenylketoouria CP):
--Grased by cehcreny af phenylalanine hy-detYylase.
—heCauseol_by ale fiecentes sn enzymes ceguirod —
we for BHy syothesix Cae ter) eee
» Gharacterized by attamulaken ol fp heaylalantae 2
be thctale ficiency te Ge Gragine ten eee ae eae esate
—. Fatdengs: .Adental Retardeben. fat (ure to_atalfe ax tal
as. tremec.& failare gre.
SS ee Sy ia:fess a ‘pid Metabolic _ eee:
a ide on: rete
ae hans bodies:
_t |Acetsne pa Ay Wer ery. Jes
2. Atet altedate os Soi
3.| B- hy derwy butyrate -
Be “npn feal. of Cells _syothesized by liver oj lathe nds
bze
falm_atety) eA in fashog -£.DM.
aol d by mest dssuec eit Cells lack mitachencee:
ere tack cazyene eee thee tr
Bile— Subst
— spe. see
SSS Car baby dates eoetabaliza= a
—Tr'ssae_lacaboa_|
ws ge
. Gluakinase & Hexokinase :—
__Gluakinase Hexakinase
whiver &. B-cey of ~Cxtra hepate.
__penlrease oe
_ + Glucose Sa ealeeteinoge et
—=highly specbe fr _ geaeml specchety
= Salvator 2
eee
—alhnily id | Lew @fhins’) ole hgh _athacty bs
Gls Chizh km) oH Ale e i)
—allocterre nat _allasteric wallihecre
—Praperly Cut tobibeted _
Ciahthtled by
__end pra duct)
_ by end-product) |
vate_kinase deficient: =
-depend__2o glycolysis to produce ATP
PR defieny results in allerahine co the BG membrane
teed | te Changes ia the Shape ERG ene ee
-Pk| _debcieng is rechrittesl ta erythray lee L pradues
I . L ~ =
Severe: beanie... hemely hte aneaive.” mi
4. Somees. fer Gluwse syrthesic Coluonergeresis)
~ 1. Pyruvate _2_ lactate Clache acid) . 3. Glucagente AA
4, Clycen| _$- preprinak (papringl aA)
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